摘要
Primary synovial sarcoma of the kidney is a rare renal malignancy. A chromosomal translocation, t(X;18), is characteristic of this disease. We report a case of primary synovial sarcoma of the kidney showing the following imaging patterns: The tumor occupied the entire left kidney, invaded into the left renal vein and inferior vena cava, and the tumor thrombus extends upward to the level of right atrium, downward to infrarenal IVC. Enlarged lymph nodes were noted in the retroperitoneum. Nodular lesions were also noted in the liver and the possibility of liver metastasis was considered. The SYT-SSX fusion transcripts associated with the t(X;18) translocation was demonstrated by RT-PCR and the diagnosis of primary synovial sarcoma was confirmed by pathology. Primary synovial sarcoma of the kidney can only be confirmed by molecular analysis. It is difficult for the radiologist to differentiate renal synovial sarcoma from other primary renal tumors by image studies. The presence of renal tumor with invasive behavior, including regional lymphadenopathy, renal vein invasion, and distant metastasis, in young adult, should alert radiologist the possibility of this unusual renal sarcoma.
原文 | English |
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頁(從 - 到) | 359-363 |
頁數 | 5 |
期刊 | Chinese Journal of Radiology |
卷 | 29 |
發行號 | 6 |
出版狀態 | Published - 12月 2004 |