Catheter ablation of ventricular tachycardia/fibrillation in a patient with right ventricular amyloidosis with initial manifestations mimicking arrhythmogenic right ventricular dysplasia/cardiomyopathy

Fa Po Chung, Yenn Jiang Lin, Ling Kuo, Shih Ann Chen*

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

7 Scopus citations

Abstract

Differentiating arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) from other cardiomyopathies is clinically important but challenging. Although the modified Task Force Criteria can facilitate diagnosis of ARVD/C according to clinical manifestations, histopathological examination plays a pivotal role in excluding other diseases that can mimic ARVD/C. Here, we report a patient with amyloidosis that initially presented similarly to ARVD/C. The diagnosis was confirmed by endomyocardial biopsy, and catheter ablation eliminated the ventricular tachyarrhythmias through an epicardial approach.

Original languageEnglish
Pages (from-to)282-285
Number of pages4
JournalKorean Circulation Journal
Volume47
Issue number2
DOIs
StatePublished - Mar 2017

Keywords

  • Amyloidosis
  • Arrhythmogenic right ventricular cardiomyopathy-dysplasia
  • Biopsy
  • Catheter ablation
  • Ventricular tachycardia

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